Pulmonary arterial capacitance index is a strong predictor for adverse outcome in children with idiopathic and heritable pulmonary arterial hypertension: methodological issues to avoid misinterpretation
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چکیده
منابع مشابه
pulmonary vascular capacitance as a predictor of vasoreactivity in idiopathic pulmonary arterial hypertension tested by adenosine
conclusions cp could be considered as an index for the prediction of vasoreactivity in patients with ipah. prediction of long-term response to calcium channel blockers in patients with ipah and a positive vasoreactive test by this index should be addressed in further studies. patients and methods fourteen patients with ipah and a vasoreactive adenosine vasoreactivity testing according to the es...
متن کاملPulmonary Vascular Capacitance as a Predictor of Vasoreactivity in Idiopathic Pulmonary Arterial Hypertension Tested by Adenosine
BACKGROUND Acute pulmonary vasoreactivity testing has been recommended in the diagnostic work-up of patients with idiopathic pulmonary arterial hypertension (IPAH). Pulmonary arteriolar capacitance (Cp) approximated by stroke volume divided by pulmonary pulse pressure (SV/PP) is considered as an independent predictor of mortality in patients with IPAH. OBJECTIVES We sought to evaluate any dif...
متن کاملHypoxemia in patients with idiopathic or heritable pulmonary arterial hypertension
BACKGROUND The prevalence and prognostic implications of hypoxemia either at rest or during six-minute walk test (6MWT) in patients with idiopathic or heritable pulmonary arterial hypertension (IPAH or HPAH) have not been systemically studied. OBJECTIVES We sought to determine the prevalence, phenotypic and prognostic implications of hypoxemia in patients with IPAH and HPAH. METHODS Patient...
متن کاملSpleen size in idiopathic and heritable pulmonary arterial hypertension.
BACKGROUND It is unknown whether the spleen size correlates with disease severity and outcome in patients with idiopathic and heritable pulmonary arterial hypertension (PAH). OBJECTIVES To determine the prevalence of splenomegaly in PAH and assess whether it correlates with severity of disease and outcome. METHODS We identified subjects with either heritable or idiopathic PAH who had Dopple...
متن کاملUnexplained iron deficiency in idiopathic and heritable pulmonary arterial hypertension.
BACKGROUND Anaemia is common in left heart failure and is associated with a poorer outcome. Many patients with pulmonary arterial hypertension (PAH) are anaemic or iron-deficient. This study was performed to investigate the prevalence of iron deficiency in PAH and to identify possible causes. METHODS All patients with idiopathic or heritable PAH diagnosed in 1995-2008 were identified. Control...
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ژورنال
عنوان ژورنال: The Journal of Pediatrics
سال: 2017
ISSN: 0022-3476
DOI: 10.1016/j.jpeds.2017.01.030